Keywords
Abstract
In the given clinical case, the patient has total pulmonary vein drainage defect, mixed type. TAPVD (total anomalous pulmonary venous drainage). Intercompartmental barrier defects have been observed together.
In the sick child, the predominance of the total drainage defect of the pulmonary vein was more pronounced. A 2-year-old patient had an intercompartmental septal defect combined with a total pulmonary vein drainage defect, and the patient did not receive medical treatment in the first years of his life. In the clinical course of the disease, symptoms of respiratory and cardiovascular insufficiency were evident, especially during physical exertion.
Clinical signs of increased pressure in the right lobe and right ventricle, insufficient blood flow to the lungs, due to failure of timely treatment of intercompartmental barrier defect combined with total pulmonary vein drainage defect. An intercompartmental barrier defect combined with a total drainage defect of the pulmonary vein was determined using an instrumental diagnostic method.
The specified endovascular method made it possible to completely eliminate changes in the lungs and its networks, to normalize pulmonary pressure. Up to 7% live with TAPVD when the defect is not corrected in time (over 20 years old). The natural course of the disease is not positive, so early surgical treatment is very necessary.